Mouse Isobutyryl-CoA dehydrogenase; mitochondrial (ACAD8) ELISA kit; ACAD-8; ARC42; FLJ22590; isobutyryl-CoA dehydrogenase; mitochondrial; acyl-Coenzyme A dehydrogenase family; member 8

For Research Use Only. Not for use in diagnostic procedures.

Store all reagents at 2-8 degree C

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Small volumes of ACAD8 elisa kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.

MBS9333282 is a ready-to-use microwell, strip plate ELISA (enzyme-linked immunosorbent assay) Kit for analyzing the presence of the acyl-Coenzyme A dehydrogenase family, member 8 (ACAD8) ELISA Kit target analytes in biological samples. The concentration gradients of the kit standards or positive controls render a theoretical kit detection range in biological research samples containing ACAD8. The ELISA analytical biochemical technique of the MBS9333282 kit is based on ACAD8 antibody-ACAD8 antigen interactions (immunosorbency) and an HRP colorimetric detection system to detect ACAD8 antigen targets in samples. The ELISA Kit is designed to detect native, not recombinant, ACAD8. Appropriate sample types may include undiluted body fluids and/or tissue homogenates, secretions. Quality control assays assessing reproducibility identified the intra-assay CV (%) and inter-assay CV(%).

45,020 Da

acyl-Coenzyme A dehydrogenase family, member 8

isobutyryl-CoA dehydrogenase, mitochondrial; ACAD-8; acyl-CoA dehydrogenase family member 8

Isobutyryl-CoA dehydrogenase, mitochondrial

ACAD-8??[Similar Products]

ACAD8_MOUSE

ACAD8: Has very high activity toward isobutyryl-CoA. Is an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Plays a role in transcriptional coactivation within the ARC complex. Defects in ACAD8 are the cause of isobutyryl-CoA dehydrogenase deficiency (IBDD). The symptoms of IBDD generally appear until late in infancy or in childhood and can include poor feeding and growth (failure to thrive), a weakened and enlarged heart (dilated cardiomyopathy), seizures, and low numbers of red blood cells (anemia). Belongs to the acyl-CoA dehydrogenase family.

Protein type: Amino Acid Metabolism - valine, leucine and isoleucine degradation; Mitochondrial; EC 1.3.99.-; Oxidoreductase

Cellular Component: mitochondrion

Molecular Function: short-branched-chain-acyl-CoA dehydrogenase activity; acyl-CoA dehydrogenase activity; FAD binding; very-long-chain-acyl-CoA dehydrogenase activity; oxidoreductase activity, acting on the CH-CH group of donors; propionyl-CoA dehydrogenase activity; oxidoreductase activity; thiol-driven fumarate reductase activity

Biological Process: metabolic process; branched chain family amino acid catabolic process

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